Isifo sikaHirschsprung singaba nezimpawu eziningana, ukubonakaliswa kwazo kuncike kakhulu kwisigaba seminyaka. Ngendlela, abafana bangakwazi ukuthola lesi sifo kunabameleli besifazane (bahlushwa lesi sifo izikhathi ezinhlanu kaningi). Izimpawu nazo ziyahlukahluka kuye ngokuthi indawo yesilonda esiswini, isikhathi sokubonakaliswa kwazo nezinkinga ezihlukahlukene ezihlobene nesifo sikaHirschsprung. Ngezansi kukhona izibonakaliso ezizenzele zona ezinganeni zeminyaka ehlukene.
Izifo Hirschsprung ezinganeni kuze kube unyaka owodwa zibonakala kanje:
- Uphawu oluyinhloko lokuhlehliswa kwesabelo se-stool kusukela ngesikhathi sokuzalwa kwengane. Kucatshangwa ukuthi kuvamile lapho isisulu sezingane ezisuka kuzalwa ngosuku lokuqala emva kokubeletha, uma lokhu kungenzeki, kufaneleke ukucabanga ngokukhona kwalesi sifo;
- Ukuvuvukala esiswini, ukuphefumula nokuphefumula;
- Izitembu ezingavamile, ukuqotshwa uma ukuhamba kwesisu kungavamile;
- Kungase kube nokuhlanza;
- Ukungabi nesifiso, ukwenqaba kwengane ukudla;
- Izingane ezinyangeni eyodwa zingabhekana nesifo sohudo;
- Ingane ihamba ngemuva kwesimiso kanye noontanga yakhe ekutholeni isisindo.
Kubantwana kusukela ngonyaka owodwa kuya kwesinye, izici ezilandelayo zesifo sikaHirschsprung zivame kakhulu:
- Ukuqotshwa okungapheli;
- Izinhlanzi zinephunga elimnandi futhi ziphuma ngebhebheni elincane. Kulesi simo, eziningi zazo aziboniswa, ngoba izinkontileka ezinkulu zamathumbu futhi aziphuthelwa.
Ngakho-ke, kungaphawulwa ukuthi kuzo zombili izigaba zeminyaka, isibonakaliso esiyinhloko sesifo sikaHirschsprung siwukuqothulwa okungapheli, okungahle kube yinto engapheli. Lesi sifo sinzima kakhulu ukubona izingane ezisanda kuzalwa, ngoba ukuncelisa ivumela isitokisini ukuba sidlule emathunjini ngokukhululekile kakhulu, kodwa ekuqaleni kokudla, ukuqothula kubonakala ngokwengeziwe, ngoba ukuvumelana kwe-stool kuyanda. Ngenxa yokuthi isihlalo sihamba ngokulibaziseka, inyama iyadakwa, okuholela ekuhlanzeni. Kufanele kuqaphele ukuthi uma lesi sifo siqhubeka siqhubeka, umphumela omncane yi-enema yokuhlanza.
Ukuvuvukala kwesigxobo esiswini - esinye isibonakaliso sesifo sikaHirschsprung, kubangelwa yi-flatulence. Lokhu kungaphawulwa, ngoba uhlobo lwalokhu luguquko lwesisu: inkaba iyadlula ngaphesheya kufanele ibe khona futhi ifana sengathi iphenduke, isisu ngokwayo sinomzimba. Amathumbu abuye abuyele eceleni.
Kodwa-ke, isifo sikaHirschsprung akuyona nje isifo sengane, singase sihlupheke ngabantu abadala. Izimbangela zesifo kubantu abadala - ukwehluleka, ukwehluleka ukuzimela kusukela ebuntwaneni, ubuhlungu emgodini wesisu ngenxa yokulibaziseka okujwayelekile ekunqandeni.
Isifo sikaHirschsprung sifaka izigaba eziningana: isigaba esikhokhelwa, isigaba esiphezulu nesincintisiwe. Iyokuqala ibonakala ngokuqothulwa kusukela ebuntwaneni, enganciphisa ngokuphumelelayo ibe yizero ngokusebenzisa ukuhlanza. Kodwa-ke, lezi zinkinga azibe zingasebenzi kahle esiteji sesibili, futhi ngenxa yalokho, isimo sesiguli siyaqhubeka, njengoba siqala ukuphuza ubuhlungu besisu, ukuphefumula. Futhi esiteji sesibili, ukugaya umzimba kuphazanyiswa futhi ukulahleka kwesisindo okubonakalayo kwenzeka. Isigaba sesithathu, esinzima kunazo zonke sibonakala ubuhlungu obungapheli nobukhulu emgodini wesisu. Ngokuzikhandla ngokomzimba futhi ukuguqula ekudleni okungavamile kwesiguli kungaholela enkingeni enjengokuvinjelwa kwamathumbu emathunjini. Ukuqeda ukuhlukumeza akukwazi ukufezwa ngezindlela ezijwayelekile: akukho ukuhlanza, akukho laxatives.
Ngandlela-thile, izinsana zingabhekana nesimo esibucayi sesifo sikaHirschsprung, futhi lesi sifo sibonakala ngokuncipha kwamathumbu emathunjini.
Indlela yokwelashwa kwalesi sifo ingenye kuphela - kungukungenelela kokuhlinzeka, okungcono kakhulu okwenziwe eminyakeni engu 2-3. Kodwa-ke, ukuhlinzekwa kuqala kunokwelashwa okulindelekile, okungenziwa ekhaya. Ukudla okhethekile kunqunywe ukuthi kuhambisana nesikhala sesiguli, okuhlanganisa ukudla okunjengama-apula, uju, i-beetroot, izaqathe, ama-porridges ahlukahlukene (i-oatmeal, i-buckwheat, njll). Kubalulekile futhi ukuba usebenzise imikhiqizo yobisi olumuncu njalo. Ukudla kunqunywe ngenhloso eyodwa: ukuhlukunyezwa okuvamile, nemikhiqizo engenhla kusiza ukuqinisa amathumbu emathunjini. Ngaphezu kokudla, ingane yesiguli inqunywe ukusikhipha isisu somzimba nesisu sokuzivocavoca esikhethekile. Kudingekile ukuthi usebenzise njalo izinhlobo ezahlukene ze-enemas, isibonelo, njenge-Vaseline, ukuhlanza, i-siphon, i-hypertonic.
Isiguli sibhekene nokuqondiswa njalo kodokotela ngomunye umnyaka nengxenye ngemuva kokusebenza. Esikhathini sokuhlolwa komtholampilo, uphinde wanikezwe ukudla okukhethekile, inkambo yokuhlanza umzimba, isethi yokuzivocavoca umzimba. Ngendlela, ukuhlanza ukuhlanza kufanele kufakwe ngesikhathi esifanayo - lokhu kuyadingeka ukuze kuthuthukiswe ukucabanga okufakiwe ukuqeda ukuphuma kwamathumbu. Phakathi nalesi sikhathi sokuvuselelwa, abazali bezingane akungabazeki nje ukuthi bazimisele ukulawula ukuhlukunyezwa kwakhe.