I-Neuralgia ye-trigeminal noma isisindo sombuso, i-arteritis yesikhashana, pheochromocytoma

I-arteritis yesikhashana iyisifo esibonakala ngokuvuvukala kwemithambo yegazi engaphakathi, igazi linikezela isikhumba. Ngendlela ejwayelekile yesifo, kukhona ukukhuluma nge-giant cell, noma i-arteritis ye-craneal. I-Neuralgia ye-trigeminal noma i-nerve facial, i-arteritis yesikhashana, pheochromocytoma - isihloko sendaba.

Isithombe sezokwelapha

Izimpawu ze-arteritis zesikhashana ziyi:

Cishe ezingxenyeni zamacala, i-arteritis yesikhashana ihambisana ne-rheumatic polymyalgia (isifo esibonakala ngobuhlungu obukhulu kanye nokuqina kobunzima behlombe nebhande elincane). Ngezinye izikhathi isithombe somtholampilo saleso sifo sinobukhulu, ngokusakazeka kwezimpawu ezinjengokukhathala, ukucindezeleka, ukukhulelwa isikhathi eside, ukulahlekelwa isisindo nesifiso. Ukuxilongwa kokuqala kwe-arteritis yesikhashana kunciphisa kakhulu ingozi yokuthuthukisa ubumpumputhe. Isisekelo sokuxilongwa yi-data yangaphandle yokuhlola kanye nemiphumela yokuhlolwa kwegazi. Lapho ehlolwa, udokotela ubhekisela ekubhekeleni kwesifo somzimba kanye nokwehla noma ukungabi khona kwe-pulsation yayo.

Ukuhlolwa

Izimbangela ze-arteritis zesikhashana azange zichazwe. Kukhona ukucabanga ukuthi lesi sifo sihlotshaniswa nempendulo yegciwane lesandulela ngculazi ezindongeni ze-arteries. Kukholelwa ukuthi indlela efanayo ehambisana nokuthuthukiswa kwe-polymyalgia ye-rheumatic. Ukulahlekelwa kombono nge-arteritis yesikhashana kungenxa ye-thrombosis yemithambo yegazi ye-retina. Ukukhubazeka okubonakalayo okubukwayo kanye nobuhlungu emhlathini kufakwe ukuvinjelwa okuyingxenye yokugeleza kwegazi. Idatha ebonisa ukuthi isifo esithathelwanayo sesifo ayitholakali. I-arteritis yesikhashana akuyona isifo esiyifa. Kodwa-ke, umehluko wobuhlanga ekubulaleni kubonisa ukuthi ukutholakala kwezakhi zofuzo kungadlala indima ekuthuthukisweni kwayo. Nge-dynamical arteritis esheshayo iyaphazamiseka ngemva kwezinsuku ezimbili noma ezintathu zokwelapha ezinezinga eliphezulu ze-steroids. Lapho engozini yokulahlekelwa umbono, ezinye izazi zincoma ukuthi ziqale ukwelashwa nge-steroids engaphakathi. Uma uthuthukisa ukuphazamiseka okubukwayo, ukuphathwa ngomlomo kwe-prednisolone ngesilinganiso esilinganiselwe sama-60 mg ngosuku kunconywa. Nge-arteritis yesikhashana, kubalulekile ukuthi ungahlehlisi ukuqaliswa kokwelashwa kuze kutholakale imiphumela ye-biopsy. I-biopsy ye-arterial kufanele yenziwe ngokushesha ngangokunokwenzeka. Phakathi nesonto lokuqala lokuphathwa kwe-steroid, imiphumela yakhe ingase ihlale ihle.

Ukulandelwa kwesikhathi eside

Emiphumeleni yokuqala emihle yokwelapha, isilinganiso se-steroids kancane kancane sinciphisa izinga lokugcina elincane (7.5-10 mg ngosuku). Lokhu kunciphisa kakhulu ingozi yemiphumela emibi ye-steroid therapy (isb., Ukuguqulwa kwamathambo noma ukunciphisa ukumelana nezifo). Kwezinye izimo, izivikeli ze-immunosuppressants (isib. I-azathioprine noma i-methotrexate) zinqunywe esikhundleni se-steroids, ikakhulukazi kulawo gulane abathinteka kakhulu ekuqedeni kwe-corticosteroids. Ukuvimbela ukuphindaphinda kwesifo kumele kuhlale iminyaka emibili.

Ukuhlola ukuphumelela kokwelashwa kwenziwa:

I-prognosis ixhomeke kakhulu ekuqaliseni kokuqala kokwelashwa. Uma kwenzeka ukukhubazeka okungathí sina okubonakalayo, amathuba okuthola kabusha ngokuphelele aphansi. Noma kunjalo, ngokumelene nemvelaphi yokwelashwa, ukuthuthukiswa okuyingxenye ekusebenzeni okubukwayo kungabonwa. Ukuqhubeka kwesi sifo ngemva kokuqala ukwelashwa kwe-steroid akunakwenzeka. Ukunciphisa umthamo we-steroids kungabangela ukuphindaphinda kwesifo. Kodwa-ke, ingozi yokuphindaphinda iyancipha ngemva kweminyaka eyodwa nengxenye yokwelapha, noma unyaka noma ngaphezulu emva kokuphela kwayo. Ukudilizwa okuphelele kuvame ukutholakala emva kweminyaka emibili kusukela ekuqaleni kokulashwa.

Ukuhlukunyezwa

I-arteritis yesikhashana ivame ukukhula kubantu abadala kuneminyaka engama-50. Abesifazane abagula kabili kaningi njengamadoda. Ukusabalalisa kwe-arteritis yesikhashana kuyahlukahluka ezweni lonke. Ngokwesilinganiso, phakathi kwabantu abaneminyaka engaphezu kwengu-50, lesi sigameko singama-0.49-23.3 amacala kubantu abayi-100 000 ngonyaka.